Search on: SPHINGOLIPID ACTIVATOR PROTEINS 
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Descriptor English:   Sphingolipid Activator Proteins 
Descriptor Spanish:   Proteínas Activadoras de Esfingolípidos 
Descriptor Portuguese:   Proteínas Ativadoras de Esfingolipídeos 
Synonyms English:   Cerebroside Sulfate Activator Protein
G(M1) Activator Protein
G(M1) Ganglioside Activating Factor
GM1 Activator Protein
Ganglioside Degradation Activator Protein
Ganglioside Hydrolysis Activator Proteins
Hexosaminidase A Activating Protein
Hexosaminidase Activating Factor  
Tree Number:   D08.211.790
Definition English:   A family of glycoprotein cofactors that are required for the efficient catabolization of SPHINGOLIPIDS by specific acid hydrolases such as GLUCOSYLCERAMIDASE; GALACTOCEREBROSIDASE; BETA-N-ACETYLHEXOSAMINIDASE; and CEREBROSIDE-SULFATASE. 
History Note English:   2005(1977) 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AG agonists AN analysis
AI antagonists & inhibitors BI biosynthesis
BL blood CF cerebrospinal fluid
CS chemical synthesis CH chemistry
CL classification DF deficiency
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UL ultrastructure UR urine
Record Number:   38689 
Unique Identifier:   D049128 

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